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New insights in peroxisomal beta-oxidation
Ferdinandusse, S.
Publication date
2002
Link to publication
Citation for published version (APA):
Ferdinandusse, S. (2002). New insights in peroxisomal beta-oxidation.
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Contents s
Abbreviations sChapterr 1 Introduction 6 Chapterr 2 Peroxisomal ^-oxidation: a review 8
Chapterr 3 Molecular cloning and expression of human carnitine 28
octanoyltransferasee (COT): evidence for its role in the peroxisomall |3-oxidation of branched-chain fatty acids
Chapterr 4 Peroxisomal fatty acid oxidation disorders and 58 kDa sterol 38
carrierr protein X (SCPx): activity measurements in liver and fibroblastss using a newly developed method
Chapterss Reinvestigation of peroxisomal 3-ketoacyl-CoA thiolase 52
deficiency:: identification of the true defect at the level of D-bifunctionall protein
Chapterr 6 Mutations in the gene encoding peroxisomal a-methylacyl-CoA 62
racemasee cause adult-onset sensory motor neuropathy
Chapterr 7 Subcellular localization and physiological role of a-methylacyl- 74
CoAA racemase
Chapterr 8 Plasma analysis of di- and trihydroxycholestanoic acid 88
diastereomerss in peroxisomal a-methylacyl-CoA racemase deficiency y
Chapterr 9 Stereochemistry of the peroxisomal branched-chain fatty acid a- 98
andd p-oxidation systems in patients suffering from different peroxisomall disorders
Chapterr 10 Identification of the peroxisomal p-oxidation enzymes involved 110
inn the biosynthesis of docosahexaenoic acid
Summaryy / Samenvatting voor iedereen 128
Dankwoordd 132 Listt of publications 135
